EP Fellows Curriculum: Arrhythmogenic Right Ventricular Cardiomyopathy: What Have we Learned in 20 Years?-ARVC

Video Transcription

Video Summary

In this video summary, Dr. Hugh Calkins discusses arrhythmogenic right ventricular dysplasia (ARVD) and its diagnosis, management, and progression. ARVD is an inherited cardiomyopathy characterized by progressive replacement of the right ventricular myocardium with fatty and fibrotic tissue. Diagnosis of ARVD requires a combination of history, physical exam, EKG, Holter monitoring, and imaging such as MRI or echo. Genetic testing is also recommended if the disease is suspected. Risk stratification for defibrillator implantation is based on factors such as history of sustained VT or sudden death, proband status, gender, and results of EP testing and Holter monitoring. Exercise restriction is a key management strategy for ARVD, as exercise can trigger arrhythmias and progression of the disease. Catheter ablation may be considered for patients with recurrent arrhythmias. Monitoring for disease progression involves regular follow-up with EKGs, Holter monitoring, and imaging. Recently, there has been a focus on the role of inflammation in ARVD, and further research is being conducted to better understand this aspect of the disease. Overall, ARVD is a progressive condition that requires ongoing monitoring and management to minimize arrhythmias and prevent disease progression.

Keywords

arrhythmogenic right ventricular dysplasia

ARVD

diagnosis

management

progression

cardiomyopathy

genetic testing

defibrillator implantation

exercise restriction

inflammation