EP Fellows Curriculum: Inherited Arrhythmic Syndromes-Inherited Arrhythmic Syndromes

Video Transcription

Video Summary

In this video, the speaker discusses various inherited arrhythmias, their management, and genetic implications. They cover topics such as acute management and inherited arrhythmias, including ventricular tachycardia and fibrillation. They also discuss inherited arrhythmia syndromes like long QT syndrome, short QT syndrome, and Brugada syndrome. The speaker emphasizes the importance of detailed clinical assessment, including personal and family history, and the role of genetic testing in identifying mutations and for cascade screening of family members. They also talk about the use of beta blockers as the treatment of choice in long QT syndrome. Additionally, they discuss other treatment options such as sympathetic denervation for refractory VF storms in long QT syndrome patients. The speaker concludes by discussing familial atrial fibrillation and the role of genetic mutations in its development. They emphasize the importance of early onset atrial fibrillation and the need for further research to understand the mechanisms of atrial fibrillation in patients with structural mutations in myocardial proteins.

Keywords

inherited arrhythmias

management

genetic implications

long QT syndrome

Brugada syndrome

genetic testing

beta blockers

treatment

atrial fibrillation