HRS Board Review 2025 New Courses (Reviewers Copy)-Workshop 1_Tomaselli_2025

Video Transcription

Video Summary

The correct approach for the patient with progressive cardiac conduction issues and myotonic dystrophy is implanting a permanent pacemaker. Myotonic dystrophy patients often experience conduction block, posing a significant risk of sudden cardiac death. The pacemaker allows the patient to safely continue myxilatin treatment for skeletal muscle disease. There's high mortality, often at a young age, due to severe ECG changes more prevalent in women. Monitoring alone isn't advisable due to unpredictable conduction issues. Supportive care for skeletal muscle disease and managing potential anesthesia complications are crucial. Sodium channel blockers and pacemakers are key in treatment plans.

Keywords

myotonic dystrophy

permanent pacemaker

cardiac conduction

sudden cardiac death

skeletal muscle disease