(FIT)-Module 1, Workshop 1: Electrocardiographic/Electrophysiologic Correlation-Tomaselli Case 10 Answer

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Video Summary

In managing myotonic dystrophy with cardiac complications, pacemaker implantation is recommended for patients like the one described, who show progressive ECG changes and benefit from medications like mexiletine. Myotonic dystrophy is associated with high sudden death rates, often due to bradycardia or tachycardia, and conduction block is common. Severe ECG abnormalities can develop unexpectedly. Supportive care and sodium channel blockers benefit skeletal muscle disease, but some medications contraindicate AV conduction issues. Backup pacing can support continued treatment. Attention is needed during surgery due to anesthesia complications, emphasizing careful management.

Keywords

myotonic dystrophy

cardiac complications

pacemaker implantation

ECG abnormalities

sodium channel blockers