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Phenotypic Differences in Genotypic Arrhythmia Cardiomyopathy Subcategories
Description
Hereditary Arrhythmogenic Cardiomyopathy (ACM) is not a uniform disease but includes classic ARVC and other subcategories. These subcategories may give rise to similar or different phenotypic manifestations. These differences may have impact on risk stratification and thus clinical relevance. A joint session with European Cardiac Arrhythmia Society (ECAS).
Learning Objectives
  • Describe the imaging differences in genotypic ACM subcategories.
  • Review the risk stratification differences in genotypic ACM subcategories.
  • Summarize the increasing impact of molecular genetics on modern advanced patient care.
Session Chair(s)
Hugh Calkins, MD
Richard Hauer, MD, PhD
Presentation
Electrocardiographic Differences in Genotypic ACM Subcategories
Presenter(s): Pyotr G. Platonov, MD, PhD

Imaging Differences in Genotypic ACM Subcategories
Presenter(s): Prachi Agarwal

Exercise Tolerance in ACM Subcategories
Presenter(s): Cynthia A. James, PhD, CGC

Risk Dependence in ACM Subcategories
Presenter(s): Julia Cadrin-Tourigny, MD, PhD

Disclosures
Pyotr Platonov:
  • Tenaya Therapeutics (Honoraria/Speaking/Consulting Fee - Membership on Advisory Committees or Review Panels)
  • Pfizer, Inc. (Honoraria/Speaking/Consulting Fee - Consulting)
Prachi Agarwal:
  • Cytokinetics (Research (Contracted Grants for PIs and Named Investigators only) - Research)
Cynthia James:
  • Lexeo, Inc. (Research (Contracted Grants for PIs and Named Investigators only) - Research)
  • Pfizer, Inc. (Honoraria/Speaking/Consulting Fee - Consulting)
  • StrideBio (Research (Contracted Grants for PIs and Named Investigators only) - Research)
  • ARVADA Therapeutics (Research (Contracted Grants for PIs and Named Investigators only) - Research)
Julia Cadrin-Tourigny:
  • Tenaya Therapeutics (Honoraria/Speaking/Consulting Fee - Consulting)
  • LEXEO Therapeutics Inc. (Honoraria/Speaking/Consulting Fee - Consulting)
  • BioMarin, Inc (Honoraria/Speaking/Consulting Fee - Consulting)

To view all Heart Rhythm 2025 Faculty Disclosures, please click here.
Education Framework
General Concepts
   --   Communication Skills and Shared Decision Making
      --   11. Know how to use decision aid tools to facilitate a shared decision regarding primary prevention implantable cardioverter-defibrillator (ICD), left atrial appendage occlusion, participation in athletics and other clinical scenarios.

Other Arrhythmia Syndromes
   --   Arrhythmogenic Cardiomyopathies
      --   270. Know how to diagnose arrhythmogenic cardiomyopathies, including the role of imaging, laboratory testing and genetic testing.
Summary
Availability: No future session
Cost: FREE
Credit Offered:
No Credit Offered
Recommended
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